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Pseudomyxoma extraperitonei in horseshoe kidney masquerading as renal hilar tumor: a case report

Authors Wang X, Gao X, Wang L, Dai Z, Fan B, Cui H, Liu Z

Received 17 August 2018

Accepted for publication 27 October 2018

Published 12 December 2018 Volume 2018:11 Pages 9027—9032


Checked for plagiarism Yes

Review by Single-blind

Peer reviewer comments 2

Editor who approved publication: Dr Sanjay Singh

Xin Wang,* Xiang Gao,* Liang Wang, Zhihong Dai, Bo Fan, Haoyu Cui, Zhiyu Liu

Department of Urology, Second Affiliated Hospital of Dalian Medical University, Dalian, Liaoning, People’s Republic of China

*These authors contributed equally to this work

Abstract: Pseudomyxoma peritonei, a rare condition consisting of intraperitoneal mucinous tumors and ascites, most commonly arises from mucinous tumors of the appendix. Very rarely, mucinous deposits arise in the retroperitoneum without intraperitoneal involvement. This has been termed pseudomyxoma extraperitonei. It is a rare and poorly understood condition that is heterogeneous in its clinical behavior, and only a few cases presenting as localized disease in the retroperitoneum have been reported. In this paper, we report the first case of pseudomyxoma extraperitonei presenting as a simple renal hilar mass and mimicking a tumor of renal origin in a horseshoe-kidney patient. The patient underwent isthmusectomy and nephrectomy. Immunohistochemical staining suggested appendiceal origin. She remained alive without adjuvant therapy postoperatively, and no evidence of recurrence was present for 25 months.

Keywords: pseudomyxoma extraperitonei, pseudomyxoma peritonei, horseshoe kidney, renal hilar tumor

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