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Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation

Authors Yagnik VD, Dawka S

Received 31 January 2019

Accepted for publication 3 April 2019

Published 25 June 2019 Volume 2019:12 Pages 279—285

DOI https://doi.org/10.2147/CEG.S203697

Checked for plagiarism Yes

Review by Single-blind

Peer reviewers approved by Dr Amy Norman

Peer reviewer comments 2

Editor who approved publication: Prof. Dr. Everson L.A. Artifon


Vipul D Yagnik,1 Sushil Dawka2

1Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, Mauritius

Abstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.

Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapy

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