Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
Received 30 November 2020
Accepted for publication 29 January 2021
Published 12 February 2021 Volume 2021:14 Pages 77—81
Checked for plagiarism Yes
Review by Single anonymous peer review
Peer reviewer comments 3
Editor who approved publication: Professor Ronald Prineas
Senai Goitom Sereke,1 Felix Bongomin,2 Geraldine Owor3
1Department of Radiology and Radiotherapy, School of Medicine, Makerere University College of Health Sciences, Kampala, Uganda; 2Department of Medical Microbiology and Immunology, Faculty of Medicine, Gulu University, Gulu, Uganda; 3Department of Pathology, School of Biomedical Sciences, Makerere University College of Health Sciences, Kampala, Uganda
Correspondence: Senai Goitom Sereke
Department of Radiology and Radiotherapy, School of Medicine, Makerere University College of Health Sciences, Kampala, Uganda
Introduction: Extramedullary hemangioblastoma is a very rare entity that has been rarely reported in the literature.
Case Presentation: A 17-year-old female presented with limping that rapidly progressed to paraparesis and urine incontinence over a one-month duration. Clinically, she had a small swelling on her spine. There was a diagnostic challenge when an enhanced magnetic resonance imaging (MRI) suggested dumbbell – shaped intradural extramedullary mass in the lower thoracic spine, hypointense on T1 and hyperintense on T2 sequences and heterointense on post contrast sequence. The radiologic differentials were pictures of nerve sheath tumors. However, histopathological examination of en bloc excisional biopsy showed hemangioblastoma with a differential of solitary fibrous tumor. Complete excision of the mass was done intraoperatively and the patient improved clinically.
Conclusion: Contrast-enhanced MRI and histopathologic correlation are important for evaluating these rare tumors.
Keywords: hemangioblastoma, solitary fibrous tumor, extramedullary, intradural-extradural, dumbbell-shaped
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